Sturge weber syndrome

Sturge Weber syndrome also known as sturge Weber Dimitri syndrome or encephalo Trigeminal angiomatosis it has port wine stain which is a facial hemangioma classical e in the distribution of the first division of fifth cranial nerve that is Trigeminal nerve the patient has focal seizures on the contralateral size and hemangiomatous changes of the meninges on the ipsilateral side as port wine stain and so calcifications develop on the ipsilateral side which are seen on the CT scan and gyriform form calcifications sturge Weber syndrome or encephalo Trigeminal angiomatosis is a congenital disease it has no genetic basis its fits are very difficult to control there may be associated contralateral hemiparesis and intellectual disability